(Congenital Megacolon; Colonic Aganglionosis)
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- Family members with the disease
- Sex: male
- Presence of Down Syndrome
- Presence of other congenital defects
- Failure to pass meconium within the first 48 hours of life (Meconium is the first bowel movement.)
- Vomiting after eating
- Swelling of abdomen
- Severe constipation for most of their lives
- Anemia—blood disorder
- Pull-through operation—The affected area of the colon is removed. The remaining healthy colon is then brought down and joined to the rectum.
- Colostomy—This may be done to allow your bowel time to rest and heal. After the affected area of colon is removed, the healthy colon is not immediately connected to the rectum. Instead, the colon is attached to an opening in the abdominal wall. Waste will then pass through this opening and into a bag outside the body. This may be done in children who are very sick or have a large portion of the colon affected.
- Closure of the colostomy—Once the area has healed, the colon will be connected to the rectum. The colostomy opening will be closed. Bowel function will gradually return to normal.
International Foundation for Functional Gastrointestinal Disorders http://www.aboutkidsgi.org
National Digestive Diseases Information Clearinghouse http://digestive.niddk.nih.gov
DynaMed Editorial Team. Hirschsprung disease. EBSCO DynaMed website. Available at: https://dynamed.ebscohost.com/about/about-us. Updated June 13, 2012. Accessed August 8, 2012.
Fecal incontinence. Pediatric Surgery Update website. Available at: http://home.coqui.net/titolugo/PSU13.htm#1361. Accessed July 24, 2012.
Hirschsprung disease. American Academy of Family Physicians Family Doctor website. Available at: http://familydoctor.org/familydoctor/en/diseases-conditions/hirschsprungs-disease.html. Accessed August 8, 2012.
National Digestive Diseases Information Clearinghouse. Hirschsprung's disease. National Digestive Diseases Information Clearinghouse website. Available at: http://digestive.niddk.nih.gov/ddiseases/pubs/hirschsprungs%5Fez/. Accessed August 8, 2012.
Surgery for children with Hirschsprung’s disease: a guide for patients and parents. University of California San Francisco website. Available at: http://www.ucsfhealth.org/childrens/edu/hirschsprung.pdf. Accessed July 24, 2012.
- Reviewer: Michael Woods, MD
- Review Date: 09/2012 -
- Update Date: 00/91/2012 -